Item Type | Name |
Academic Article
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Lack of Clinical Hypersensitivity to Penicillin Antibiotics in Common Variable Immunodeficiency.
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Academic Article
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Prevalence of Granulomas in Patients With Primary Immunodeficiency Disorders, United States: Data From National Health Care Claims and the US Immunodeficiency Network Registry.
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Academic Article
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TH1 and TH2 cytokine mRNA and protein levels in human immunodeficiency virus (HIV)-seropositive and HIV-seronegative youths.
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Academic Article
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HIV/AIDS in Hawai'i: state of the state.
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Concept
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Acquired Immunodeficiency Syndrome
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Concept
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Wiskott-Aldrich Syndrome
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Concept
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Severe Combined Immunodeficiency
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Concept
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Common Variable Immunodeficiency
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Concept
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Wiskott-Aldrich Syndrome Protein
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Concept
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X-Linked Combined Immunodeficiency Diseases
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Academic Article
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Phenotypic characterization of patients with rheumatologic manifestations of common variable immunodeficiency.
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Academic Article
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Progressive neurodegeneration in patients with primary immunodeficiency disease on IVIG treatment.
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Academic Article
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Diminished T cell numbers in patients with chronic granulomatous disease.
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Academic Article
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Uncommon conundrum in common variable immunodeficiency.
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Academic Article
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Pondering probiotics.
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Academic Article
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Pediatric common variable immunodeficiency: immunologic and phenotypic associations with switched memory B cells.
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Academic Article
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Genome-wide association identifies diverse causes of common variable immunodeficiency.
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Academic Article
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A patient with X-linked dyskeratosis congenita presenting with bronchiolitis obliterans requiring lung transplantation and immunodeficiency.
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Academic Article
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A single-center study of hematopoietic stem cell transplantation for primary immune deficiencies (PIDD).
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Academic Article
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Chronic non-bacterial osteomyelitis in a patient with common variable immunodeficiency.
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Academic Article
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Terminal deletion of 11q with significant late-onset combined immune deficiency.
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Academic Article
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USIDNET: a strategy to build a community of clinical immunologists.
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Academic Article
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Multicenter experience in hematopoietic stem cell transplantation for serious complications of common variable immunodeficiency.
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Academic Article
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Exome sequencing analysis reveals variants in primary immunodeficiency genes in patients with very early onset inflammatory bowel disease.
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Academic Article
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Transplantation outcomes for severe combined immunodeficiency, 2000-2009.
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Academic Article
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Rare variants at 16p11.2 are associated with common variable immunodeficiency.
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Academic Article
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Association of CLEC16A with human common variable immunodeficiency disorder and role in murine B cells.
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Academic Article
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Health care utilization by patients with common variable immune deficiency defined by International Classification of Diseases, Ninth Revision code 279.06.
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Academic Article
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Broad-spectrum antibodies against self-antigens and cytokines in RAG deficiency.
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Academic Article
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Primary Immunodeficiency Diseases: an Update on the Classification from the International Union of Immunological Societies Expert Committee for Primary Immunodeficiency 2015.
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Academic Article
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Severe, persistent, and fatal T-cell immunodeficiency following therapy for infantile leukemia.
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Academic Article
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Immunodeficiencies Associated with Abnormal Newborn Screening for T Cell and B Cell Lymphopenia.
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Academic Article
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Identification of 22q11.2 Deletion Syndrome via Newborn Screening for Severe Combined Immunodeficiency.
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Academic Article
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Two Sides of the Same Coin: Pediatric-Onset and Adult-Onset Common Variable Immune Deficiency.
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Academic Article
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Immune reconstitution and survival of 100 SCID patients post-hematopoietic cell transplant: a PIDTC natural history study.
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Academic Article
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Novel ZBTB24 Mutation Associated with Immunodeficiency, Centromere Instability, and Facial Anomalies Type-2 Syndrome Identified in a Patient with Very Early Onset Inflammatory Bowel Disease.
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Academic Article
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International Union of Immunological Societies: 2017 Primary Immunodeficiency Diseases Committee Report on Inborn Errors of Immunity.
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Academic Article
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Common Variable Immunodeficiency Non-Infectious Disease Endotypes Redefined Using Unbiased Network Clustering in Large Electronic Datasets.
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Academic Article
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Low Serum IgE Is a Sensitive and Specific Marker for Common Variable Immunodeficiency (CVID).
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Academic Article
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Complications Associated with Underweight Primary Immunodeficiency Patients: Prevalence and Associations Within the USIDNET Registry.
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Academic Article
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Patients with common variable immunodeficiency with autoimmune cytopenias exhibit hyperplastic yet inefficient germinal center responses.
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Academic Article
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Cancer in primary immunodeficiency diseases: Cancer incidence in the United States Immune Deficiency Network Registry.
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Academic Article
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Autoimmune Cytopenias and Associated Conditions in CVID: a Report From the USIDNET Registry.
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Academic Article
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Low Rates of Poliovirus Antibodies in Primary Immunodeficiency Patients on Regular Intravenous Immunoglobulin Treatment.
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Academic Article
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SCID genotype and 6-month posttransplant CD4 count predict survival and immune recovery.
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Academic Article
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Rubella Virus-Associated Cutaneous Granulomatous Disease: a Unique Complication in Immune-Deficient Patients, Not Limited to DNA Repair Disorders.
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Academic Article
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Diagnostic interpretation of genetic studies in patients with primary immunodeficiency diseases: A?working group report of the Primary Immunodeficiency Diseases Committee of the American Academy of Allergy, Asthma & Immunology.
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Academic Article
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Prophylactic Antibiotics Versus Immunoglobulin Replacement in Specific Antibody Deficiency.
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Academic Article
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Neutropenia as a sign of immunodeficiency.
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Academic Article
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Hematopoietic stem cell transplantation for CD40 ligand deficiency: Results from an EBMT/ESID-IEWP-SCETIDE-PIDTC study.
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Academic Article
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Common variable immunodeficiency-associated endotoxemia promotes early commitment to the T follicular lineage.
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Academic Article
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Infectious vaccine-derived rubella viruses emerge, persist, and evolve in cutaneous granulomas of children with primary immunodeficiencies.
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Academic Article
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Hematopoietic Cell Transplantation in Patients With Primary Immune Regulatory Disorders (PIRD): A Primary Immune Deficiency Treatment Consortium (PIDTC) Survey.
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Academic Article
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Lymphoproliferative Disease in CVID: a Report of Types and Frequencies from a US Patient Registry.
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Academic Article
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European Society for Immunodeficiencies (ESID) and European Reference Network on Rare Primary Immunodeficiency, Autoinflammatory and Autoimmune Diseases (ERN RITA) Complement Guideline: Deficiencies, Diagnosis, and Management.
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Academic Article
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Excellent outcomes following hematopoietic cell transplantation for Wiskott-Aldrich syndrome: a PIDTC report.
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Academic Article
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The scary world of variants of uncertain significance (VUS): A?hitchhiker's guide to interpretation.
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Academic Article
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Global systematic review of primary immunodeficiency registries.
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Academic Article
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Focus on increasing treatment self-efficacy to improve human immunodeficiency virus treatment adherence.
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Academic Article
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Adenosine Deaminase (ADA)-Deficient Severe Combined Immune Deficiency (SCID) in the US Immunodeficiency Network (USIDNet) Registry.
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Academic Article
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Rubella virus-associated chronic inflammation in primary immunodeficiency diseases.
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Academic Article
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PROMIS-29 survey confirms major impact of fatigue on health-related quality of life in common variable immunodeficiency.
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Academic Article
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Infection Phenotypes Among Patients with Primary Antibody Deficiency Mined from a US Patient Registry.
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Academic Article
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Persons Living With Primary Immunodeficiency Act as Citizen Scientists and Launch Prospective Cohort Body Temperature Study.
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Academic Article
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The Ever-Increasing Array of Novel Inborn Errors of Immunity: an Interim Update by the IUIS Committee.
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Academic Article
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Heterozygous OAS1 gain-of-function variants cause an autoinflammatory immunodeficiency.
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Academic Article
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Self-Limited COVID-19 in a Patient with Artemis Hypomorphic SCID.
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Academic Article
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The relevance of primary immunodeficiency registries on a global perspective.
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Academic Article
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The diagnosis of severe combined immunodeficiency: Implementation of the PIDTC 2022 Definitions.
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Academic Article
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Ocular Manifestations in Primary Immunodeficiency Disorders: A Report From the United States Immunodeficiency Network (USIDNET) Registry.
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Academic Article
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Risk Factors of Pneumonia in Primary Antibody Deficiency Patients Receiving Immunoglobulin Therapy: Data from the US Immunodeficiency Network (USIDNET).
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Academic Article
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Morbidity, Mortality, and Therapeutics in Combined Immunodeficiency: Data From the USIDNET Registry.
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Academic Article
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Measuring the effect of newborn screening on survival after haematopoietic cell transplantation for severe combined immunodeficiency: a 36-year longitudinal study from the Primary Immune Deficiency Treatment Consortium.
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Academic Article
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A patient with Pitt-Hopkins syndrome with concomitant common variable immunodeficiency.
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Academic Article
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Difficult Cases in Primary Immunodeficiency.
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Academic Article
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Who's your data? Primary immune deficiency differential diagnosis prediction via machine learning and data mining of the USIDNET registry.
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Academic Article
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Respiratory Comorbidities Associated with Bronchiectasis in Patients with Common Variable Immunodeficiency in the USIDNET Registry.
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